hrp0086p1-p42 | Adrenal P1 | ESPE2016

Acute Lysis of a Giant Pediatric Adrenal Cortical Carcinoma Following One Dose of op’DDD

Motte Emmanuelle , Rothenbuhler Anya , Durand Philippe , Bougneres Pierre

Background: op’DDD can be used in adrenal cortical carcinoma (ACC) i) when surgery is impossible ii) or as an adjunct to surgery when local extension or metastases are present.Objectives and hypotheses: To report the unexpected spectacular effects of op’DDD in an unoperable ACC.Patient and results: A 3-year-old black African girl presented in poor shape with a 2-year history of pubic hair, clitoromegaly, abdominal distens...